GLA Polyclonal Antibody

Elabscience
Product Code: E-AB-67013
Product Group: Primary Antibodies
Supplier: Elabscience
CodeSizePrice
E-AB-67013-60uL60uL£210.00
Quantity:
E-AB-67013-120uL120uL£291.00
Quantity:
E-AB-67013-200uL200uL£431.00
Quantity:
Prices exclude any Taxes / VAT

Overview

Host Type: Rabbit
Antibody Isotype: IgG
Antibody Clonality: Polyclonal
Regulatory Status: RUO
Target Species:
  • Human
  • Mouse
Applications:
  • Immunofluorescence (IF)
  • Western Blot (WB)
Shipping:
Ice packs
Storage:
Store at -20°C. Avoid freeze / thaw cycles.

Images

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Immunofluorescence analysis of HeLa cells using Galactosidase alpha (Galactosidase alpha (GLA)) Polyclonal Antibody Blue: DAPI for nuclear staining.

Immunofluorescence analysis of HeLa cells using Galactosidase alpha (Galactosidase alpha (GLA)) Polyclonal Antibody Blue: DAPI for nuclear staining.

Documents

Further Information

Abbreviation:
GLA
Background:
This gene encodes a homodimeric glycoprotein that hydrolyses the terminal alpha-galactosyl moieties from glycolipids and glycoproteins. This enzyme predominantly hydrolyzes ceramide trihexoside, and it can catalyze the hydrolysis of melibiose into galactose and glucose. A variety of mutations in this gene affect the synthesis, processing, and stability of this enzyme, which causes Fabry disease, a rare lysosomal storage disorder that results from a failure to catabolize alpha-D-galactosyl glycolipid moieties.
Buffer:
PBS with 0.02% sodium azide,50% glycerol,pH7.3.
Calculated MW:
48kDa
Concentration:
1 mg/mL
Conjugation:
Unconjugated
Dilution:
WB 1:500-1:2000,IF 1:50-1:100
Immunogen:
Recombinant fusion protein of human GLA
ObservedMW:
49kDa
Purification method:
Affinity purification
Target Synonym:
GLA;GALA
UNIProt ID:
P06280