L2HGDH Polyclonal Antibody

Elabscience
Product Code: E-AB-63179
Product Group: Primary Antibodies
Supplier: Elabscience
CodeSizePrice
E-AB-63179-60uL60uL£210.00
Quantity:
E-AB-63179-120uL120uL£291.00
Quantity:
E-AB-63179-200uL200uL£431.00
Quantity:
Prices exclude any Taxes / VAT

Overview

Host Type: Rabbit
Antibody Isotype: IgG
Antibody Clonality: Polyclonal
Regulatory Status: RUO
Target Species:
  • Human
  • Mouse
Application: Western Blot (WB)
Shipping:
Ice packs
Storage:
Store at -20°C. Avoid freeze / thaw cycles.

Images

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Western blot analysis of extracts of various cell lines using L2HGDH Polyclonal Antibody at 1:1000 dilution.

Western blot analysis of extracts of various cell lines using L2HGDH Polyclonal Antibody at 1:1000 dilution.

Documents

Further Information

Abbreviation:
L2HGDH
Background:
This gene encodes L-2-hydroxyglutarate dehydrogenase, a FAD-dependent enzyme that oxidizes L-2-hydroxyglutarate to alpha-ketoglutarate in a variety of mammalian tissues. Mutations in this gene cause L-2-hydroxyglutaric aciduria, a rare autosomal recessive neurometabolic disorder resulting in moderate to severe mental retardation.
Buffer:
PBS with 0.02% sodium azide,50% glycerol,pH7.3.
Calculated MW:
48kDa/50kDa
Concentration:
1 mg/mL
Conjugation:
Unconjugated
Dilution:
WB 1:500-1:2000
Immunogen:
Recombinant fusion protein of human L2HGDH
ObservedMW:
40kDa
Purification method:
Affinity purification
Target Synonym:
L2HGDH;C14orf160;L2HGA
UNIProt ID:
Q9H9P8