BCKDHB Polyclonal Antibody
| Code | Size | Price |
|---|
| E-AB-90197-60uL | 60uL | £210.00 |
Quantity:
| E-AB-90197-120uL | 120uL | £291.00 |
Quantity:
| E-AB-90197-200uL | 200uL | £431.00 |
Quantity:
Prices exclude any Taxes / VAT
Overview
Host Type: Rabbit
Antibody Isotype: IgG
Antibody Clonality: Polyclonal
Regulatory Status: RUO
Target Species: Mouse
Application: Western Blot (WB)
Shipping:
Ice packs
Storage:
Store at -20°C. Avoid freeze/thaw cycles.
Further Information
Abbreviation:
BCKDHB
Background:
This gene encodes the E1 beta subunit of branched-chain keto acid dehydrogenase, which is a multienzyme complex associated with the inner membrane of mitochondria. This enzyme complex functions in the catabolism of branched-chain amino acids. Mutations in this gene have been associated with maple syrup urine disease (MSUD), type 1B, a disease characterized by a maple syrup odor to the urine in addition to mental and physical retardation and feeding problems. Alternative splicing at this locus results in multiple transcript variants.
Buffer:
PBS with 0.02% sodium azide,50% glycerol,pH7.3.
Calculated MW:
23kDa/43kDa
Concentration:
1mg/mL
Conjugation:
Unconjugated
Dilution:
WB 1:500-1:2000
Immunogen:
Recombinant fusion protein of human BCKDHB
ObservedMW:
43kDa
Purification method:
Affinity purification
Target Synonym:
BCKDHB;BCKDE1B;BCKDH E1-beta;E1B;BCKDHE1-beta
UNIProt ID:
P21953