HADHSC Antibody
| Code | Size | Price |
|---|
| PSI-XW-8005-0.05mg | 0.05mg | £801.00 |
Quantity:
Prices exclude any Taxes / VAT
Overview
Host Type: Chicken
Antibody Clonality: Polyclonal
Regulatory Status: RUO
Target Species:
- Human
- Mouse
- Rat
Application: Western Blot (WB)
Storage:
HADHSC antibody can be stored at 4˚C for short term (weeks). Long term storage should be at -20˚C. As with all antibodies care should be taken to avoid repeated freeze thaw cycles. Antibodies should not be exposed to prolonged high temperatures.
Documents
Further Information
Additional Names:
HAD, HADHSC, SCHAD, Hydroxyacyl-coenzyme A dehydrogenase, mitochondrial, Medium and short-chain L-3-hydroxyacyl-coenzyme A dehydrogenase, HCDH, Short chain 3hydroxyacylCoA dehydrogenase, Medium and short chain L-3-hydroxyacyl-coenzyme A dehydrogenase
Application Note:
Short chain 3-hydroxyacyl-CoA dehydrogenase, mitochondrial antibody can be used for the detection of Short chain 3-hydroxyacyl-CoA dehydrogenase, mitochondrial by Western Blot.
Background:
FUNCTION: Plays an essential role in the mitochondrial β-oxidation of short chain fatty acids. Exerts it highest activity toward 3-hydroxybutyryl-CoA.
DISEASE: Defects in HADHSC are the cause of 3-α-hydroxyacyl-CoA dehydrogenase deficiency (HAD deficiency) [MIM:609609]. HAD deficiency is a metabolic disorder with various clinical presentations including hypoglycemia, hepatoencephalopathy, myopathy or cardiomyopathy, and in some cases sudden death.
DISEASE: Defects in HADHSC are the cause of 3-α-hydroxyacyl-CoA dehydrogenase deficiency (HAD deficiency) [MIM:609609]. HAD deficiency is a metabolic disorder with various clinical presentations including hypoglycemia, hepatoencephalopathy, myopathy or cardiomyopathy, and in some cases sudden death.
Buffer:
Phosphate-Buffered Saline. No preservatives added.
Concentration:
1 mg/mL
Conjugate:
Unconjugated
DISCLAIMER:
Optimal dilutions/concentrations should be determined by the end user. The information provided is a guideline for product use. Optimal dilutions/concentrations should be determined by the end user. The information provided is a guideline for product use. This product is for research use only.
Immunogen:
57-314
NCBI Gene ID #:
3033
NCBI Official Name:
hydroxyacyl-CoA dehydrogenase
NCBI Official Symbol:
HADH
NCBI Organism:
Homo sapiens
Physical State:
Liquid
PREDICTED MOLECULAR WEIGHT:
34.3 kDa (calculated)
Protein Accession #:
NP_005318.1
Protein GI Number:
4885387
Purification:
Immunoaffinity Purified
Swissprot #:
Q16836
User NOte:
Optimal dilutions for each application to be determined by the researcher.