FKRP Antibody
| Code | Size | Price |
|---|
| PSI-57-619-400ul | 400ul | £626.00 |
Quantity:
Prices exclude any Taxes / VAT
Overview
Host Type: Rabbit
Antibody Isotype: Rabbit Ig
Antibody Clonality: Polyclonal
Regulatory Status: RUO
Target Species: Human
Application: Western Blot (WB)
Storage:
Store at 4˚C for three months and -20˚C, stable for up to one year. As with all antibodies care should be taken to avoid repeated freeze thaw cycles. Antibodies should not be exposed to prolonged high temperatures.
Documents
Further Information
Additional Names:
Fukutin-related protein, 2---, FKRP
Application Note:
For WB starting dilution is: 1:1000
Background:
This gene encodes a protein which is targeted to the
medial Golgi apparatus and is necessary for posttranslational
modification of dystroglycan. Mutations in this gene have been
associated with congenital muscular dystrophy, mental retardation,
and cerebellar cysts. Several alternatively spliced transcript
variants of this gene have been described, but the full-length
nature of some of these variants has not been determined. [provided
by RefSeq].
Background References:
- Kawahara, G., et al. Hum. Mol. Genet. 19(4):623-633(2010)
- Crowther-Swanepoel, D., et al. Nat. Genet. 42(2):132-136(2010)
- Lu, P.J., et al. Biochim. Biophys. Acta 1802(2):253-258(2010)
- Hanisch, F., et al. J. Neurol. 257(2):300-301(2010)
Buffer:
Supplied in PBS with 0.09% (W/V) sodium azide.
Concentration:
batch dependent
Conjugate:
Unconjugated
DISCLAIMER:
Optimal dilutions/concentrations should be determined by the end user. The information provided is a guideline for product use. This product is for research use only.
Immunogen:
This FKRP antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 237-265 amino acids from the Central region of human FKRP.
NCBI Gene ID #:
79147
NCBI Official Name:
Fukutin-related protein
NCBI Official Symbol:
FKRP
NCBI Organism:
Homo sapiens
Physical State:
Liquid
PREDICTED MOLECULAR WEIGHT:
55 kDa
Protein Accession #:
Q9H9S5
Protein GI Number:
46395992
Purification:
This antibody is purified through a protein A column, followed by peptide affinity purification.
Research Area:
Signal Transduction
Swissprot #:
Q9H9S5
User NOte:
Optimal dilutions for each application to be determined by the researcher.